MeSH Browser

MeSH Supplementary: Congenital lobar emphysema
Unique ID: C535735
RDF Unique Identifier: http://id.nlm.nih.gov/mesh/C535735
Entry Term(s): Emphysema, congenital lobar
Registry Number: 0
Heading Mapped to: Pulmonary Emphysema / *congenital
Frequency: 117
Note: A hereditary autosomal dominant form of emphysema that presents in infancy and is characterized by hyperinflation of the affected lobe; compression of surrounding normal lung tissue, and hypoplasia of the bronchial tissue. OMIM: 130710
Date of Entry: 2010/08/25
Revision Date: 2015/08/18

Congenital lobar emphysema MeSH Supplementary Concept Data 2023