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Dentinogenesis Imperfecta MeSH Descriptor Data 2026
An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.
Entry Term(s)
Capdepont Teeth
Dentinogenesis Imperfecta 1
Dentinogenesis Imperfecta without Osteogenesis Imperfecta
An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.