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Glycogen Storage Disease Type VI MeSH Descriptor Data 2023


MeSH Heading
Glycogen Storage Disease Type VI
Tree Number(s)
C16.320.565.202.449.580
C18.452.648.202.449.580
Unique ID
D006013
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D006013
Scope Note
A hepatic GLYCOGEN STORAGE DISEASE in which there is an apparent deficiency of hepatic phosphorylase (GLYCOGEN PHOSPHORYLASE, LIVER FORM) activity.
Entry Version
GLYCOGEN STORAGE DIS VI
Entry Term(s)
Glycogenosis 6
Glycogenosis Type VI
Glycogenosis VI
Hepatic Glycogen Phosphorylase Deficiency
Hers Disease
Hers' Disease
Liver Phosphorylase Deficiency Syndrome
Previous Indexing
Glucosyltransferases/metabolism (1966-1974)
Glycogenosis (1966-1974)
Liver Diseases (1966-1974)
See Also
Glycogen Phosphorylase, Liver Form
Public MeSH Note
91; was see under GLYCOGEN STORAGE DISEASE 1989-90; was GLYCOGENOSIS 6 see under GLYCOGENOSIS 1975-88
Online Note
use GLYCOGEN STORAGE DISEASE TYPE VI to search GLYCOGENOSIS 6 1975-88
History Note
91(89); was see under GLYCOGEN STORAGE DISEASE 1989-90; was GLYCOGENOSIS 6 see under GLYCOGENOSIS 1975-88
Date Established
1991/01/01
Date of Entry
1974/12/12
Revision Date
2013/07/08
Glycogen Storage Disease Type VI Preferred
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