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Ornithine Carbamoyltransferase MeSH Descriptor Data 2026


MeSH Heading
Ornithine Carbamoyltransferase
Tree Number(s)
D08.811.913.555.275.600
Unique ID
D009954
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D009954
Scope Note
A urea cycle enzyme that catalyzes the formation of orthophosphate and L-citrulline (CITRULLINE) from CARBAMOYL PHOSPHATE and L-ornithine (ORNITHINE). Deficiency of this enzyme may be transmitted as an X-linked trait. EC 2.1.3.3.
Entry Term(s)
Ornithine Carbamylphosphate Transferase
Ornithine Transcarbamylase
Registry Numbers
EC 2.1.3.3
Related Numbers
9001-69-8
CAS Type 1 Name
Carbamoyl-phosphate:L-ornithine carbamoyltransferase
See Also
Ornithine Carbamoyltransferase Deficiency Disease
Public MeSH Note
1965
History Note
1965(1964)
Entry Combination
deficiency:Ornithine Carbamoyltransferase Deficiency Disease
Date Introduced
1965/01/01
Last Updated
2009/07/06
Ornithine Carbamoyltransferase Preferred
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