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Sturge-Weber Syndrome MeSH Descriptor Data 2023


MeSH Heading
Sturge-Weber Syndrome
Tree Number(s)
C04.557.645.375.850
C10.562.800
C14.907.077.850
Unique ID
D013341
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D013341
Scope Note
A non-inherited congenital condition with vascular and neurological abnormalities. It is characterized by facial vascular nevi (PORT-WINE STAIN), and capillary angiomatosis of intracranial membranes (MENINGES; CHOROID). Neurological features include EPILEPSY; cognitive deficits; GLAUCOMA; and visual defects.
Entry Term(s)
Angiomatosis Oculoorbital-Thalamic Syndrome
Encephalofacial Hemangiomatosis Syndrome
Meningo-Oculo-Facial Angiomatosis
Meningofacial Angiomatosis-Cerebral Calcification Syndrome
Neuroretinoangiomatosis
Parkes Weber Syndrome
Parkes-Weber Syndrome
Phakomatosis, Sturge-Weber
Sturge Disease
Sturge Syndrome
Sturge's Syndrome
Sturge-Kalischer-Weber Syndrome
Sturge-Weber-Dimitri Syndrome
Sturge-Weber-Krabbe Syndrome
Public MeSH Note
91; was see under ANGIOMATOSIS 1975-90; DIMITRI DISEASE was see STURGE-WEBER SYNDROME 1989-93
Online Note
search ANGIOMATOSIS 1966-74; use STURGE-WEBER SYNDROME to search DIMITRI DISEASE 1989-93
History Note
91(75); was see under ANGIOMATOSIS 1975-90; DIMITRI DISEASE was see STURGE-WEBER SYNDROME 1989-93
Date Established
1991/01/01
Date of Entry
1999/01/01
Revision Date
2013/07/08
Sturge-Weber Syndrome Preferred
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