- Concept UI
- M0027463
- Scope Note
- A variety of rare sarcoma having a reticulated fibrous stroma enclosing groups of sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled with connective tissue. It is a rare tumor, usually occurring between 15 and 35 years of age. It appears in the muscles of the extremities in adults and most commonly in the head and neck regions of children. Though slow-growing, it commonly metastasizes to the lungs, brain, bones, and lymph nodes. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1365)
- Terms
-
Sarcoma, Alveolar Soft Part
Preferred Term
Term UI
T054511
Date01/01/1999
LexicalTag
NON
ThesaurusID
NLM (1994)
-
Alveolar Soft Part Sarcoma
Term UI
T752461
Date06/08/2009
LexicalTag
NON
ThesaurusID
-
Alveolar Soft-Part Sarcoma
Term UI
T812104
Date11/15/2011
LexicalTag
NON
ThesaurusID
OMIM (2013)