- Concept UI
- M0501042
- Scope Note
- A subtype of Ehlers-Danlos syndrome (EDS) characterized by vascular pathologies, e.g., AORTIC DISSECTION in addition to common EDS findings, e.g., hyperextensible skin and joints, skin fragility and reduced wound healing capability. It is associated with mutations in collagen type III alpha 1 chain gene (COLLAGEN TYPE III).
- Terms
-
Ehlers-Danlos Syndrome, Type IV
Preferred Term
Term UI
T680130
Date08/24/2006
LexicalTag
ACR
ThesaurusID
NLM (2008)
-
Ehlers Danlos Syndrome, Sack-Barabas Type
Term UI
T834230
Date12/12/2012
LexicalTag
ACR
ThesaurusID
ORD (2010)
-
Type IV Ehlers-Danlos Syndrome
Term UI
T001119668
Date04/08/2022
LexicalTag
ACX
ThesaurusID
NLM (2023)
-
Vascular Type Ehlers-Danlos Syndrome
Term UI
T001119669
Date04/08/2022
LexicalTag
ACR
ThesaurusID
NLM (2023)
-
Ehlers-Danlos Syndrome, Vascular Type
Term UI
T680131
Date08/24/2006
LexicalTag
ACR
ThesaurusID
-
Ehlers-Danlos Syndrome, Arterial Type
Term UI
T812206
Date11/15/2011
LexicalTag
NON
ThesaurusID
OMIM (2013)
-
Ehlers-Danlos Syndrome, Ecchymotic Type
Term UI
T812209
Date11/15/2011
LexicalTag
ACR
ThesaurusID
OMIM (2013)
-
Ehlers-Danlos Syndrome, Sack-Barabas Type
Term UI
T812210
Date11/15/2011
LexicalTag
NON
ThesaurusID
OMIM (2013)
-
EDS IV
Term UI
T824492
Date06/21/2012
LexicalTag
ABB
ThesaurusID
OMIM (2013)
-
Ehlers-Danlos Syndrome, Type IV, Autosomal Dominant
Term UI
T824493
Date06/21/2012
LexicalTag
EPO
ThesaurusID
OMIM (2013)
-
Ehlers Danlos Syndrome Type 4, Autosomal Dominant
Term UI
T834227
Date12/12/2012
LexicalTag
ACR
ThesaurusID
ORD (2010)
-
Ehlers Danlos Syndrome, Arterial Type
Term UI
T834228
Date12/12/2012
LexicalTag
ACR
ThesaurusID
ORD (2010)
-
Ehlers Danlos Syndrome, Ecchymotic Type
Term UI
T834229
Date12/12/2012
LexicalTag
ACR
ThesaurusID
ORD (2010)
-
Vascular Ehlers-Danlos Syndrome
Term UI
T001119706
Date04/08/2022
LexicalTag
ACX
ThesaurusID
NLM (2023)