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Caroli Disease MeSH Descriptor Data 2026


MeSH Heading
Caroli Disease
Tree Number(s)
C06.130.120.127.500
C06.198.184.500
C16.131.077.245.250
C16.131.314.184.500
C16.320.184.250
Unique ID
D016767
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D016767
Scope Note
Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.
Entry Version
CAROLI DIS
Entry Term(s)
Caroli Syndrome
Caroli's Disease
Caroli's Syndrome
Previous Indexing
Bile Duct Diseases/congenital (1966-1992)
Bile Ducts, Intrahepatic/abnormalities (1985-1992)
Biliary Dyskinesia (1966-1984)
Public MeSH Note
2004; see CAROLI'S DISEASE 1993-2003
History Note
2004 (1993)
Date Introduced
1993/01/01
Last Updated
2026/01/01
Caroli Disease Preferred
Caroli's Syndrome Related
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