- Concept UI
- M0028167
- Scope Note
- Similar to MEN2A, it is also caused by mutations of the MEN2 gene, also known as the RET proto-oncogene. Its clinical symptoms include medullary carcinoma (CARCINOMA, MEDULLARY) of THYROID GLAND and PHEOCHROMOCYTOMA of ADRENAL MEDULLA (50%). Unlike MEN2a, MEN2b does not involve PARATHYROID NEOPLASMS. It can be distinguished from MEN2A by its neural abnormalities such as mucosal NEUROMAS on EYELIDS; LIP; and TONGUE, and ganglioneuromatosis of GASTROINTESTINAL TRACT leading to MEGACOLON. It is an autosomal dominant inherited disease.
- Terms
-
Multiple Endocrine Neoplasia Type 2b
Preferred Term
Term UI
T056067
Date01/01/1999
LexicalTag
NON
ThesaurusID
NLM (1995)
-
Multiple Endocrine Neoplasia, Type 2b
Term UI
T751066
Date05/13/2009
LexicalTag
NON
ThesaurusID
-
Multiple Endocrine Neoplasms Type 2b
Term UI
T056068
Date04/01/1994
LexicalTag
NON
ThesaurusID
NLM (1995)
-
Neoplasia, Multiple Endocrine Type 2b
Term UI
T056066
Date04/01/1994
LexicalTag
NON
ThesaurusID
NLM (1995)
-
Neoplasms, Multiple Endocrine Type 2b
Term UI
T056069
Date04/01/1994
LexicalTag
NON
ThesaurusID
NLM (1995)
-
Neuromata, Mucosal, With Endocrine Tumors
Term UI
T811748
Date11/15/2011
LexicalTag
NON
ThesaurusID
OMIM (2013)
-
Wagenmann-Froboese Syndrome
Term UI
T782999
Date12/29/2010
LexicalTag
EPO
ThesaurusID
-
Multiple Endocrine Neoplasia, Type IIb
Term UI
T825014
Date06/26/2012
LexicalTag
NON
ThesaurusID
OMIM (2013)
-
MEN IIb
Term UI
T056073
Date04/01/1994
LexicalTag
ABB
ThesaurusID
-
MEN III
Term UI
T056065
Date04/01/1994
LexicalTag
ABB
ThesaurusID
NLM (1995)
-
MEN2b
Term UI
T056075
Date04/01/1994
LexicalTag
ABB
ThesaurusID
-
MEA 2b
Term UI
T056071
Date04/01/1994
LexicalTag
ABB
ThesaurusID
NLM (1995)
-
MEA IIb
Term UI
T056074
Date04/01/1994
LexicalTag
ABB
ThesaurusID
NLM (1995)
-
MEN 2b
Term UI
T056070
Date04/01/1994
LexicalTag
ABB
ThesaurusID
NLM (1995)
-
Mucosal Neuroma Syndrome
Term UI
T056076
Date04/01/1994
LexicalTag
NON
ThesaurusID
-
MEN 3
Term UI
T056072
Date04/01/1994
LexicalTag
ABB
ThesaurusID
NLM (1995)