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UDPglucose-Hexose-1-Phosphate Uridylyltransferase MeSH Descriptor Data 2026


MeSH Heading
UDPglucose-Hexose-1-Phosphate Uridylyltransferase
Tree Number(s)
D08.811.913.696.445.850
Unique ID
D006599
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D006599
Annotation
/defic: consider GALACTOSEMIAS
Scope Note
An enzyme that catalyzes the transfer of UMP from UDPglucose to galactose 1-phosphate, forming UDPgalactose and glucose 1-phosphate. Deficiency in this enzyme is the major cause of GALACTOSEMIA. EC 2.7.7.12.
Entry Term(s)
Galactose-1-P-Uridyltransferase
Hexosephosphate Uridylyltransferase
Phosphogalactose Uridyl Transferase
Uridyl Transferase
Registry Numbers
EC 2.7.7.12
Related Numbers
9026-21-5
CAS Type 1 Name
UDPglucose:alpha-D-galactose-1-phosphate uridylyltransferase
Previous Indexing
Galactose (1970-1974)
Hexosephosphates (1970-1974)
Nucleotidyltransferases (1970-1974)
Uridine Diphosphate Sugars (1970-1974)
See Also
Galactosemias
Public MeSH Note
98; see HEXOSEPHOSPHATE URIDYLYLTRANSFERASE 1991-97; see NUCLEOTIDYLTRANSFERASES 1975-90
History Note
98(75)
Date Introduced
1991/01/01
Last Updated
2018/07/01
UDPglucose-Hexose-1-Phosphate Uridylyltransferase Preferred
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