- Concept UI
- M0011165
- Scope Note
- A condition that is caused by HYPERPLASIA of LYMPHOCYTES in the small intestine (INTESTINE, SMALL) and the mesenteric LYMPH NODES. These lymphocytes produce an anomalous alpha heavy chain protein. Generally, these IPSID patients have either concurrent LYMPHOMA or develop lymphoma within a few years. The disease was first described in the Mediterranean region and is characterized by malabsorption; WEIGHT LOSS; DIARRHEA; and STEATORRHEA.
- Terms
-
Immunoproliferative Small Intestinal Disease
Preferred Term
Term UI
T021485
Date01/01/1999
LexicalTag
NON
ThesaurusID
NLM (1987)
-
Lymphoma, Mediterranean
Term UI
T021487
Date06/24/1986
LexicalTag
EPO
ThesaurusID
UNK (19XX)
-
alpha-Chain Disease
Term UI
T021483
Date06/24/1986
LexicalTag
NON
ThesaurusID
UNK (19XX)
-
Heavy Chain Disease, IgA Type
Term UI
T021484
Date06/24/1986
LexicalTag
NON
ThesaurusID
UNK (19XX)
-
IPSID
Term UI
T021486
Date06/24/1986
LexicalTag
ABB
ThesaurusID
UNK (19XX)