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Insomnia, Fatal Familial MeSH Descriptor Data 2023


MeSH Heading
Insomnia, Fatal Familial
Tree Number(s)
C01.207.800.392
C10.228.228.800.392
C10.574.843.512
C10.886.425.800.800.400
Unique ID
D034062
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D034062
Scope Note
An autosomal dominant disorder characterized by degeneration of the THALAMUS and progressive insomnia. It is caused by a mutation in the prion protein (PRIONS).
Entry Term(s)
Familial Fatal Insomnia
Fatal Familial Insomnia
Insomnia Familial Fatal
Previous Indexing
Prion Diseases (1992-2002)
Sleep Initiation and Maintenance Disorders (1986-1992)
Public MeSH Note
2003; see PRION DISEASES 1993-2002
History Note
2003; use PRION DISEASES 1993-2002
Date Established
2003/01/01
Date of Entry
2002/07/03
Revision Date
2019/06/17
Insomnia, Fatal Familial Preferred
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