- Concept UI
- M0020849
- Scope Note
- A degenerative disease of the central nervous system characterized by balance difficulties; OCULAR MOTILITY DISORDERS (supranuclear ophthalmoplegia); DYSARTHRIA; swallowing difficulties; and axial DYSTONIA. Onset is usually in the fifth decade and disease progression occurs over several years. Pathologic findings include neurofibrillary degeneration and neuronal loss in the dorsal MESENCEPHALON; SUBTHALAMIC NUCLEUS; RED NUCLEUS; pallidum; dentate nucleus; and vestibular nuclei. (From Adams et al., Principles of Neurology, 6th ed, pp1076-7)
- Terms
-
Supranuclear Palsy, Progressive
Preferred Term
Term UI
T039601
Date01/01/1999
LexicalTag
NON
ThesaurusID
-
Palsy, Progressive Supranuclear
Term UI
T039600
Date04/01/1986
LexicalTag
NON
ThesaurusID
UNK (19XX)
-
Progressive Supranuclear Palsy
Term UI
T842339
Date04/18/2013
LexicalTag
NON
ThesaurusID
GHR (2014)
-
Richardson's Syndrome
Term UI
T842340
Date04/18/2013
LexicalTag
EPO
ThesaurusID
GHR (2014)
-
Steele-Richardson-Olszewski Disease
Term UI
T364587
Date11/03/1999
LexicalTag
EPO
ThesaurusID
NLM (2000)
-
Steele-Richardson-Olszewski Syndrome
Term UI
T039599
Date04/01/1986
LexicalTag
EPO
ThesaurusID