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Wiskott-Aldrich Syndrome MeSH Descriptor Data 2023


MeSH Heading
Wiskott-Aldrich Syndrome
Tree Number(s)
C15.378.100.100.970
C15.378.463.960
C15.378.553.546.605.900
C16.320.099.970
C16.320.322.937
C16.320.798.875
C20.673.627.900
C20.673.795.875
Unique ID
D014923
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D014923
Scope Note
A rare, X-linked immunodeficiency syndrome characterized by ECZEMA; LYMPHOPENIA; and, recurrent pyogenic infection. It is seen exclusively in young boys. Typically, IMMUNOGLOBULIN M levels are low and IMMUNOGLOBULIN A and IMMUNOGLOBULIN E levels are elevated. Lymphoreticular malignancies are common.
Entry Term(s)
Aldrich Syndrome
Eczema-Thrombocytopenia-Immunodeficiency Syndrome
Imd2
Immunodeficiency 2
Wiskott Syndrome
Public MeSH Note
85; was ALDRICH SYNDROME 1963-84
Online Note
use WISKOTT-ALDRICH SYNDROME to search ALDRICH SYNDROME 1966-84
History Note
85; was ALDRICH SYNDROME 1963-84
Date Established
1985/01/01
Date of Entry
1999/01/01
Revision Date
2019/06/17
Wiskott-Aldrich Syndrome Preferred
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