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1-Pyrroline-5-Carboxylate Dehydrogenase MeSH Descriptor Data 2023


MeSH Heading
1-Pyrroline-5-Carboxylate Dehydrogenase
Tree Number(s)
D08.811.682.662.693
Unique ID
D050842
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D050842
Scope Note
An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.
Entry Term(s)
Delta(1)-Pyrroline-5-Carboxylate Dehydrogenase
GGS Dehydrogenase
Glutamic-Gamma-Semialdehyde Dehydrogenase
Glutamyl-Gamma-Semialdehyde Dehydrogenase
NADP+ Specific 8-Glutamate Semialdehyde Dehydrogenase
Registry Number
EC 1.2.1.88
Related Numbers
9054-82-4
Public MeSH Note
2006; 1-PYRROLINE-5-CARBOXYLATE DEHYDROGENASE was indexed under AMINE OXIDOREDUCTASES 1981-2004
History Note
2006(1981)
Date Established
2006/01/01
Date of Entry
2005/06/30
Revision Date
2016/06/02
1-Pyrroline-5-Carboxylate Dehydrogenase Preferred
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