- Concept UI
- M0076387
- Related Numbers
- 37274-61-6
- Scope Note
- A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
- Terms
-
Isovaleryl-CoA Dehydrogenase
Preferred Term
Term UI
T106390
Date01/01/1955
LexicalTag
NON
ThesaurusID
NLM (2006)
-
Isovaleryl CoA Dehydrogenase
Term UI
T106388
Date01/01/1955
LexicalTag
NON
ThesaurusID
NLM (2006)
-
Isovaleryl-Coenzyme A Dehydrogenase
Term UI
T106389
Date01/01/1955
LexicalTag
NON
ThesaurusID
NLM (2006)