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Basal Cell Nevus Syndrome MeSH Descriptor Data 2021


MeSH Heading
Basal Cell Nevus Syndrome
Tree Number(s)
C04.182.089.530.690.150
C04.557.470.200.165.150
C04.557.470.565.165.150
C04.700.175
C05.116.099.105
C05.500.470.690.150
C07.320.450.670.130
C16.131.077.130
C16.320.700.175
Unique ID
D001478
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D001478
Annotation
coordinate IM with precoordinated organ/neoplasm (IM or NIM) only if pertinent; do not confuse entry term GORLIN-GOLTZ SYNDROME with GOLTZ- GORLIN SYNDROME see FOCAL DERMAL HYPOPLASIA
Scope Note
Hereditary disorder consisting of multiple basal cell carcinomas, odontogenic keratocysts, and multiple skeletal defects, e.g., frontal and temporoparietal bossing, bifurcated and splayed ribs, kyphoscoliosis, fusion of vertebrae, and cervicothoracic spina bifida. Genetic transmission is autosomal dominant.
Entry Term(s)
Fifth Phacomatosis
Gorlin Syndrome
Gorlin-Goltz Syndrome
Multiple Basal Cell Nevi, Odontogenic Keratocysts, and Skeletal Anomalies
NBCCS
Nevoid Basal Cell Carcinoma Syndrome
Nevus Syndrome, Basal Cell
Previous Indexing
Bone Cyst (1966-1979)
Carcinoma, Basal Cell (1966-1979)
Jaw Diseases (1967-1979)
Jaw Neoplasms (1967-1979)
Skin Neoplasms (1967-1979)
Syndrome (1972-1979)
specific jaw disease (1967-1979)
specific jaw neoplasm (1967-1979)
Public MeSH Note
91; was see under CARCINOMA, BASAL CELL 1980-90
History Note
91(80); was see under CARCINOMA, BASAL CELL 1980-90
Date Established
1991/01/01
Date of Entry
1979/04/25
Revision Date
2013/07/08
Basal Cell Nevus Syndrome Preferred
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