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Incontinentia Pigmenti MeSH Descriptor Data 2021


MeSH Heading
Incontinentia Pigmenti
Tree Number(s)
C16.131.077.445
C16.131.831.580
C16.320.850.420
C17.800.621.497
C17.800.804.580
C17.800.827.420
Unique ID
D007184
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/D007184
Annotation
multiple skin & other abnorm; do not confuse with INCONTINENTIA PIGMENTI ACHROMIANS see PIGMENTATION DISORDERS
Scope Note
A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
Entry Term(s)
Bloch-Siemens Syndrome
Bloch-Siemens-Sulzberger Syndrome
Bloch-Sulzberger Syndrome
Previous Indexing
Pigmentation Disorders (1966-1986)
Public MeSH Note
91; was see under PIGMENTATION DISORDERS 1987-90
History Note
91(87); was see under PIGMENTATION DISORDERS 1987-90
Date Established
1991/01/01
Date of Entry
1986/04/03
Revision Date
2016/07/01
Incontinentia Pigmenti Preferred
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